EJVES Extra
Volume 13, Issue 2 , Pages 9-12, February 2007

Spontaneous Non-traumatic Rupture of a Non-aneurysmatic Infrarenal Abdominal Aorta in a 10-Year Old Girl without Histological Evidence of Connective Tissue or Autoimmune Disease: A Case Report

  • R.A. Pol

      Affiliations

    • Department of Surgery, Isala Klinieken, Zwolle, The Netherlands
  • ,
  • H.A.J.M. Kurvers

      Affiliations

    • Department of Surgery, University Medical Center, St Radboud, Nijmegen, The Netherlands
  • ,
  • J.B.G.M. Verheij

      Affiliations

    • Department of Genetics, University Medical Center Groningen, The Netherlands
  • ,
  • G. Pals

      Affiliations

    • Department of Clinical Genetics, VU Medical Center Amsterdam, The Netherlands
  • ,
  • A.M. van der Wal

      Affiliations

    • Department of Pathology, University Medical Center, Amsterdam, The Netherlands
  • ,
  • J. Boers

      Affiliations

    • Department of Pathology, Isala Klinieken, Zwolle, The Netherlands
  • ,
  • P.J.G. Jörning

      Affiliations

    • Department of Surgery, Isala Klinieken, Zwolle, The Netherlands
    • Corresponding Author InformationCorresponding author. P.J.G. Jörning, Department of surgery, Isala Clinics, Dr. van Heesweg 2, 8025 AB Zwolle, The Netherlands.

Accepted 30 July 2006.

Spontaneous non-traumatic rupture of a non-aneurysmatic infrarenal abdominal aorta is an extremely rare condition, which to our knowledge, has only been described in adults. Rupture is usually associated with some form of connective tissue or autoimmune disease, which causes weakness of the aortic tunica media. This report is the first to present a case of a non-traumatic rupture of a non-aneurysmatic abdominal aorta in a 10-year old girl. Histological investigation of microscopic sections of the ruptured aorta, molecular biological, and DNA mutation analyses, did not demonstrate any abnormalities.

Keywords: Abdominal aorta, Spontaneous rupture, Connective tissue disease, Autoimmune disease, Child

 

PII: S1533-3167(06)00071-9

doi:10.1016/j.ejvsextra.2006.07.005

EJVES Extra
Volume 13, Issue 2 , Pages 9-12, February 2007